Proptosis as Initial Presentation of an Ethmoid Ossifying Fibroma in Pediatric Age

Abstract

Ossifying fibroma is an uncommon benign bone tumor, whose most frequent location is the maxillofacial bones, but its origin in the ethmoid sinus is rare.  The highest incidence is described between the second and fourth decades of life. A review of the national literature on ethmoid ossifying fibromas with orbital extension was carried out, and no published reports were found. We present the case of a 10 year old female patient who was referred to Oculoplasty consultation for noticing left ocular protrusion for three months. Ultrasound, computed tomography and magnetic resonance imaging showed a tumor lesion of the ethmoidal sinus with involvement of the left orbit causing proptosis, with imaging characteristics suggestive of a probable ossifying fibroma. Nasal endoscopic biopsy confirmed the diagnosis.